Disnea típica en un paciente con diagnóstico atípico
Typical dyspnea in a patient with an atypical diagnosis
Rev. am. med. respir; 24 (2), 2024
Publication year: 2024
El sarcoma primario de arteria pulmonar es un tumor poco frecuente y con muy mal pronóstico. Su incidencia es difícil de estimar. Presenta una sintomatología inespecífica que dificulta y retrasa su diagnóstico. Presentamos un paciente de 62 años diagnostica do inicialmente de tromboembolismo pulmonar con una clínica discordante. Se decide continuar el estudio, que confirma posteriormente el diagnóstico de sarcoma primario de arteria pulmonar mediante biopsia(AU)
Primary pulmonary artery sarcoma is a rare tumor with a very poor prognosis. Its inci dence is hard to estimate. It presents with nonspecific symptoms, delaying the diagnosis and making it challenging. We present a 62-year-old patient initially diagnosed with pulmonary thromboembolism, exhibiting discordant symptoms. Further investigation was pursued, ultimately confirming the diagnosis of primary pulmonary artery sarcoma through biopsy(AU)