Results: 13

Congenital Langerhans cell histiocytosis: a good prognosis disease?

An. bras. dermatol; 92 (5,supl.1), 2017
Abstract: Langerhans cell histiocytosis is rare and more frequent in children. The skin is affected in 50% of the cases and is the only site in 10%. Its course varies from self-limited and localized forms to severe multisystemic forms. Congenital cases are usually exclusively cutaneous and self-limited, ...

Hemophagocytic syndrome: pitfalls in its diagnosis

Säo Paulo med. j; 115 (5), 1997
The hemophagocytic syndrome (HS) is characterized by a clinical picture of fever, hepatospienomegaly, lymphadenopathy and peripheral pancytopenia. The morphologic hallmark of this syndrome is the phagocytosis of hematopoietic elements by morphologically normal macrophages. HS is considered rare and may b...