Abstract Objectives: to describe the clinical epidemiological and care profiles of pediatric patients with sickle cell disease. Methods: a descriptive study of all (48) children and adolescents with sickle cell disease, assisted at a public referral hospital in Paraíba State. The information were obta...
Abstract Objective: To evaluate the cognitive abilities of children and adolescents with sickle cell anemia diagnosed through neonatal screening and to compare them with healthy controls, adjusting the results to their socioeconomic status. Methods: Cognitive assessment was performed with the Wechsler ...
ABSTRACT Objective: The aim of this study was to determine the effect of hydroxyurea on adverse clinical events and haematological indices in paediatric patients with sickle cell anaemia. Method: This study compared the same cohort of patients before and after hydroxyurea therapy, monitoring the rate o...
La infección por parvovirus B19 humano, es la causa de la mayor parte de los casos de crisis aplásica transitoria que aparecen de forma brusca en pacientes con enfermedades hemolíticas crónicas, como es el caso de la drepanocitosis. Por otra parte, se han descrito unos pocos casos de infección aguda...
ABSTRACT Objective: To determine if sickle cell disease (SCD) bone pain crisis is mitigated by use of an angiotensin-converting enzyme inhibitor (ACEI), following a case report of ACEIs preventing bone pain crisis. Methods: Patients with SCD who attended the Haematology Clinic at Jos University Teachin...
La anemia de células falciformes (ACF) es una patología con altos índices de complicaciones; además, cuando se presenta durante el embarazo su manejo se convierte en un desafío médico debido al riesgo elevado de morbimortalidad materna y perinatal. A continuación, se hace una breve rev...
ABSTRACT Objective: To know the main health guidance needs of family members of children with sickle cell disease. Method: Qualitative research, developed in a pediatric reference hospital of Ceará State, between April and May 2017, through the participation of 12 family members of children with sickl...
Sickle cell anemia was a rare disease in Chile, especially in adults, however the recent immigration wave from Haiti is changing this scenario. We report a 29 year old black female from Haiti with a non-disclosed history of sickle cell anemia. She was transfused with two units of red blood cells, found u...
ABSTRACT Objective: To identify self-care demands of men with sickle cell disease and priapism and describe self-care measures in light of Orem's Self-Care Theory. Method: This is a descriptive exploratory study with qualitative approach conducted with nine men with a history of sickle cell disease and...
Introducción: El estado inflamatorio que acompaña la anemia drepanocítica puede asociarse a amiloidosis sistémica, complicación que ha sido comunicada en esta enfermedad, que también puede afectar los nervios periféricos por el proceso vaso-oclusivo crónico en esta. Objetivos: Evaluar la función...
