Results: 72

Hidrocefalia Congénita: Síndrome de Gómez-López-Hernández, un síndrome subdiagnosticado. Caso clínico

Rev. chil. pediatr; 89 (1), 2018
Resumen: Introducción: Las hidrocefalias son condiciones complejas influenciadas por factores genéticos y ambientales. Excluyendo las hidrocefalias adquiridas por infección o tumores encefálicos, las hidrocefalias congénitas de causa genética pueden ocurrir de forma aislada (hidrocefalia aislada,...

Do you know this syndrome? Ascher´s syndrome: clinical findings of little known triad

An. bras. dermatol; 92 (5), 2017
Abstract: Ascher's syndrome consists of double lip, blepharochalasis and sometimes non-toxic thyroid enlargement. It is a rare, benign, rarely reported, and sometimes misdiagnosed condition that most often affects patients under 20 years old. The etiology remains unknown, although factors such as trauma,...

Abordagem cirúrgica do hiperteleorbitismo na displasia craniofrontonasal

Rev. Col. Bras. Cir; 44 (4), 2017
RESUMO Objetivo: apresentar nossa experiência no tratamento cirúrgico do hiperteleorbitismo na displasia craniofrontonasal. Métodos: análise retrospectiva dos pacientes com displasia craniofrontonasal operados por orbital box osteotomy ou por bipartição facial entre os anos de 1997 e 2015. Inform...

Modificaciones cefalométricas esqueletales en pacientes Clase II División 1 tratados con Aparatología Bimler
Skeletals cefalometrics changes in Class II Division 1 patients treated with Bimler Appliance

Introducción: Durante el crecimiento y desarrollo del niño pueden aparecer desarmonías esqueletales a nivel del macizo cráneo-facial. Entre estas se encuentra el Síndrome de Clase ll División 1, siendo el avance mandibular una de las alternativas para su corrección. Con este fin el Dr. Bimler dise...

Aspectos psicológicos relacionados ao indivíduo com fissura labiopalatal: uma revisão de literatura

Rev. Salusvita (Online); 36 (4), 2017
Introdução: as fissuras labiopalatais pertencem ao grupo de anomalias orofaciais, caracterizadas por uma fenda labial e/ou palatal na parte superior da boca, uni ou bilateral. Na literatura, as fissuras apresentam alta prevalência e podem interferir negativamente na vida dos pacientes e familiares, ca...

Diagnosis of infant synostotic and nonsynostotic cranial deformities: a review for pediatricians

Rev. paul. pediatr; 34 (4), 2016
Abstract Objective: To review the current comprehensive care for nonsyndromic craniosynostosis and nonsynostotic cranial deformity and to offer an overall view of these craniofacial conditions. Data source: The review was conducted in the PubMed, SciELO, and LILACS databases without time or language re...

Craniofacial anomalies associated with hypospadias. Description of a hospital based population in South America

Int. braz. j. urol; 42 (4), 2016
ABSTRACT Introduction: Hypospadias is a congenital abnormality of the penis, in which there is incomplete development of the distal urethra. There are numerous reports showing an increase of prevalence of hypospadias. Association of craniofacial malformations in patients diagnosed with hypospadias is ra...

Conductas de riesgo en adolescentes con patología crónica compleja bajo control en un policlínico de un hospital pediátrico de Santiago

Rev. méd. Chile; 144 (6), 2016
Adolescents with complex diseases may have a higher frequency of risk behaviors than their healthy peers. Aim: To characterize risk behaviors in adolescents with complex chronic diseases. Patients and Methods: Risk behaviors were assessed by means of a self-administered questionnaire designed for this pu...