Results: 178

Brazilian Consensus for the Treatment of Multiple Sclerosis: Brazilian Academy of Neurology and Brazilian Committee on Treatment and Research in Multiple Sclerosis

Arq. neuropsiquiatr; 76 (8), 2018
ABSTRACT The expanding therapeutic arsenal in multiple sclerosis (MS) has allowed for more effective and personalized treatment, but the choice and management of disease-modifying therapies (DMTs) is becoming increasingly complex. In this context, experts from the Brazilian Committee on Treatment and Res...

Fibrosis pulmonar aguda asociada a intoxicación por Paraquat: caso clínico

Rev. méd. Chile; 146 (7), 2018
Paraquat, a non-selective bipyridyl pesticide, is one of the leading causes of death from intoxication in many parts of Asia and America. It is the second most sold herbicide worldwide, being widely used in Chile. Its ingestion generates toxicity due to the release of superoxide radicals, mainly affectin...

Effect of conversion from calcineurin inhibitors to everolimus on hepatitis C viremia in adult kidney transplant recipients

J. bras. nefrol; 40 (2), 2018
ABSTRACT Introduction: Currently, there is no specific immunosuppressive protocol for hepatitis C (HCV)-positive renal transplants recipients. Thus, the aim of this study was to evaluate the conversion effect to everolimus (EVR) on HCV in adult kidney recipients. Method: This is an exploratory single-c...

Tuberous sclerosis complex: review based on new diagnostic criteria

An. bras. dermatol; 93 (3), 2018
Abstract: Tuberous sclerosis complex is a multisystemic, autosomal dominant genetic disorder with complete penetrance, that can evolve with hamartomas in multiple organs, such as skin, central nervous system, kidney and lung. Due to the wide phenotypic variability, the disease is often not recognized. Tu...

Taquicardia persistente en mujer joven deportista

Rev. chil. cardiol; 37 (1), 2018
Resumen: Una mujer joven, deportista, evoluciona con compromiso del estado general y síntomas constitucionales, asociado a taquicardia persistente y baja de peso de casi un año de evolución, con laboratorio, electrocardiograma y ecocardiograma inicialmente anodinos....

Dermatomiositis juvenil: experiencia de 13 años en un hospital de atención terciaria. Análisis de 17 casos clínicos

Arch. pediatr. Urug; 89 (2), 2018
La dermatomiositis juvenil (DMJ) es una miopatía inflamatoria adquirida de base inmunológica acompañada por alteraciones cutáneas características. El objetivo de este artículo es describir las características clínicas y exámenes complementarios de un grupo de 17 pacientes con diagnóstico de DMJ...

Síndrome urémico hemolítico atípico recurrente post-trasplante renal: tratamiento con eculizumab
Recurrent atypical hemolytic uremic syndrome after renal transplantation: treatment with eculizumab

Medicina (B.Aires); 78 (2), 2018
El síndrome urémico hemolítico atípico (SUHa) es una entidad rara que se presenta como una microangiopatía trombótica (anemia hemolítica no inmune, trombocitopenia e insuficiencia renal aguda), cuyas lesiones anatomopatológicas típicas son el engrosamiento de las paredes de capilares y arteriola...

Ustequinumabe para o tratamento de pacientes adultos com artrite psoriásica ativa que apresentaram resposta inadequada aos medicamentos modificadores do curso da doença

CONTEXTO: A artrite psoriásica (AP) é uma artrite inflamatória crônica que afeta ligamentos, tendões, fáscias, articulações axiais e periféricas e está associada à psoríase cutânea. No Brasil, o Protocolo Clínico e Diretriz Terapêutica (PCDT) do Ministério da Saúde de 2017 estabelece o t...

McArdle's disease: an underestimated or underdiagnosed myopathy in rheumatologic practice? Cases series and literature review

OBJECTIVE: McArdle's disease is a metabolic myopathy that manifests with varied clinical conditions and is often confounded with other diagnoses. Herein, the authors report a case series and carry out a literature review. METHODS: A cross-sectional single-center study evaluating 12 patients with McArdle...