LILACS – Literatura Latinoamericana y del Caribe de Ciencias de la Salud

Familial "benign" pemphigus? Erythroderma and fatal outcome

Tansini, Paula Baldissera; Boff, Ana Letícia; Weber, Magda Blessmann; Bonamigo, Renan Rangel.

An. bras. dermatol; 95 (1), 2020

Abstract Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual...

Acantólisis/patología, Infecciones Relacionadas con Catéteres, Dermatitis Exfoliativa/complicaciones, Dermatitis Exfoliativa/tratamiento farmacológico, Dermatitis Exfoliativa/patología, Resultado Fatal, Persona de Mediana Edad, Pénfigo Familiar Benigno/complicaciones, Pénfigo Familiar Benigno/tratamiento farmacológico, Pénfigo Familiar Benigno/patología

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Pemphigus foliaceus as a differential diagnosis in vesicobullous lesions

ABSTRACT Given the challenge of clinical diagnosis of bullous skin lesions, this report aimed to discuss the histological changes, the presentation and clinical reasoning for diagnosis of these lesions. At the same time, the importance of the pathology was reviewed to identify these clinical scenarios. I...