Results: 4

Adult linear IgA bullous dermatosis: report of three cases

An. bras. dermatol; 93 (3), 2018
Abstract: Linear immunoglobulin A bullous dermatosis is a rare autoimmune disease that usually has an excellent prognosis in childhood; however, its control is more difficult in adults. It presents heterogeneous clinical manifestations and is frequently confused with other bullous diseases such as bullou...

Linear IgA and IgG bullous dermatosis

An. bras. dermatol; 91 (5,supl.1), 2016
Abstract Childhood linear immunoglobulin A dermatosis is a rare autoimmune vesiculobullous disease. It results in linear deposition of autoantibodies (immunoglobulin A) against antigens in the basal membrane zone, leading to subepidermal cleavage. Additional depositions of immunoglobulin G and complement...

Vancomycin-associated linear IgA disease mimicking toxic epidermal necrolysis

An. bras. dermatol; 91 (5,supl.1), 2016
Abstract Linear IgA dermatosis is a rare subepidermal autoimmune blistering disease characterized by linear deposition of IgA along the basement membrane zone. In the last three decades, many different drugs have been associated with the drug-induced form of the disease, especially vancomycin. We report ...

Dermatosis ampollar por inmunoglobulina A lineal: Reporte de dos casos

Arch. argent. pediatr; 113 (5), 2015
La dermatosis ampollar por inmunoglobulina A lineal es una rara enfermedad, generalmente autolimitada, que afecta a niños de 4,5 años (edad media), con una incidencia de 0,52,3 casos/millón de habitantes/año. Es, tras la dermatitis herpetiforme, la enfermedad ampollar pediátrica más frecuente. Ocur...