Niemann-Pick disease type B: HRCT assessment of pulmonary involvement
J. bras. pneumol; 43 (6), 2017
ABSTRACT Objective: To analyze HRCT findings in patients with Niemann-Pick disease (NPD) type B, in order to determine the frequency of HRCT patterns and their distribution in the lung parenchyma, as well as the most common clinical characteristics. Methods: We studied 13 patients (3 males and 10 femal...