Extensive pyoderma gangrenosum-like lesions revealing a case of hyperzincemia and hypercalprotectinemia: when to suspect it?
An. bras. dermatol; 94 (6), 2019
Abstract Hyperzincemia and hypercalprotectinemia is a rare inflammatory disease caused by a mutation in the PSTPIP1 gene, with a dysregulation of calprotectin metabolism. Calprotectin is a zinc-binding protein with antimicrobial properties and pro-inflammatory action. The authors report the case of a 20 ...
Ciclosporina/uso terapéutico, Fármacos Dermatológicos/uso terapéutico, Glucocorticoides/uso terapéutico, Complejo de Antígeno L1 de Leucocito/sangre, Errores Innatos del Metabolismo de los Metales/tratamiento farmacológico, Errores Innatos del Metabolismo de los Metales/patología, Prednisolona/uso terapéutico, Piodermia Gangrenosa/patología, Resultado del Tratamiento, Zinc/sangre