Results: 7

Ultrastructural aspects of the skin in lipoid proteinosis (Urbach-Wiethe disease)

An. bras. dermatol; 96 (6), 2021
Abstract Lipoid proteinosis is a rare autosomal recessive disease, characterized by hyaline deposits of PAS-positive material in tissues due to mutations in the ECM1 gene. This study evaluated the ultrastructure of the skin of a 6-year-old child affected by this condition. The light microscopy identified...

X-radiation does not affect the dental pulp: a morphological study in rats

Introduction: Radiotherapy is one of the methods used as a treatment for malignant tumors in the head and neck region and it can cause tissue damage in the irradiated areas. In head and neck radiotherapy, teeth are often included within the irradiation area and, consequently, the dental pulp; which recei...

Follicular dendritic cell sarcoma aggravated by hyaline-vascular Castleman's disease in association with paraneoplastic pemphigus: study of the tumor and successful treatment

An. bras. dermatol; 94 (5), 2019
Abstract The authors have successfully treated and monitored a case of paraneoplastic pemphigus in association with follicular dendritic cell sarcoma aggravated by hyaline-vascular Castleman's disease. The patient was a 56-year-old female who presented with recalcitrant erosive lichen planus of the oral ...

Is it always blepharitis? Urbach-Wiethe syndrome (lipoid proteinosis)

Arq. bras. oftalmol; 82 (3), 2019
ABSTRACT A 12-year-old girl presented with recurrent crusty debris and dandruff at the base of both eyelashes despite having completed different medical treatments. She had had a hoarse voice since her early childhood. Upon anterior segment examination of the eyes, we found yellow-white, bead-like papule...

Cirrose e deficiência de Alfa1-Antitripsina: estudo clinicopatológico de dois casos com análise ultra-estrutural
Cirrhosis and alpha-1 antitrypsin deficiency: clinico-pathological study of two cases with ultraestructural analysis

J. bras. med; 62 (3), 1992
Aspectos clinicolaboratoriais e achados na microscopia óptica e eletrônica do fígado de duas pacientes idosas com cirrose e deficiência de alfa1-antitripsia näo -suspeitada foram relatados. Foram encontradas inclusöes eosinofílicas PAS-positivas e diastase-resistentes nos hepatócitos ao exame his...