Results: 10

Informe de caso de miocardiopatía no compactada en una mujer de 34 años

Introducción: la miocardiopatía no compactada (MCNC) es una miocardiopatía no clasificada por la Organización Mundial de la Salud. Se describe como una enfermedad congénita muy rara, donde se observan trabeculaciones endomiocárdicas que aumentan en número y prominencia. Esta miocardiopatía con...

Miocardiopatia não compactada em crianças e adolescentes: do desafio do diagnóstico ecocardiográfico ao acompanhamento clínico

ABC., imagem cardiovasc; 34 (4), 2021
Fundamentos: Miocardiopatia não compactada (MCNC) caracteriza-se por hipertrabeculações e recessos profundos no ventrículo esquerdo, com apresentação clínica heterogênea, desde pacientes assintomáticos a insuficiência cardíaca (IC), eventos tromboembólicos arritmias com risco de morte súbita...

Left ventricular noncompaction in a Para athlete

Einstein (Säo Paulo); 17 (2), 2019
ABSTRACT The left ventricular noncompaction is a congenital cardiomyopathy characterized by the presence of abnormal trabeculations in the left ventricle. The present study describes the case of a 14-year-old female Para athlete, who plays goalball. She was asymptomatic, with history of congenital nystag...

Fetal noncompaction cardiomyopathy and histologic diagnosis of spongy myocardium: case report and review of the literature

Abstract Noncompaction cardiomyopathy (NCCM) and left ventricular noncompaction (LVNC), in their isolated form, are rare cardiomyopathies. They are characterized by a thickened myocardium due to the presence of deep trabeculae recesses, and to thick trabeculae. This condition is associated with a variabl...

A Rare Case of Non-compaction Cardiomyopathy in an Indo-Caribbean Patient

West Indian med. j; 67 (1), 2018
ABSTRACT Non-compaction cardiomyopathy is a rare form of cardiac disease that presents with symptoms of congestive heart failure, ventricular arrhythmias or thromboembolism. Within the Caribbean setting, there are limited data regarding its existence. We present a case of non-compaction cardiomyopathy, d...

Miocardiopatía no-compacta biventricular

Rev. costarric. cardiol; 18 (1/2), 2016
ResumenLa miocardiopatía ventricular no compacta (NCVI) es una afección rara con alta morbilidad y mortalidad debido a arritmias malignas, embolia trombótica sistémica e insuficiencia cardíaca. Se cree que la NCVI es causada por una interrupción en el proceso normal de compactación miocárdica. La...