Autoimmune pancreatitis is a characteristic manifestation of the spectrum of the disease related to IgG4, a rare autoimmune disorder that presents clinically with obstructive jaundice due to the infiltration of plasma cells and fibrosis in the pancreas. There may be other symptoms in case of involvement ...
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Enfermedades del Sistema Digestivo,
Enfermedades Pancreáticas,
Pancreatitis Autoinmune,
Enfermedades del Sistema Inmune,
Enfermedades Autoinmunes,
Enfermedad Relacionada con Inmunoglobulina G4,
Enfermedades Hematológicas y Linfáticas,
Enfermedades Hematológicas,
Trastornos de las Plaquetas Sanguíneas,
Trombocitopenia
Immunoglobulin G4 (IgG4-RD) -related disease is a regional or systemic fibroinflammatory disease of unknown etiology. It has a characteristic histopathological appearance of dense lymphoplasmacytic infiltrates with abundant IgG4 positive plasma cells, storiform fibrosis and obliterative phlebitis with th...
La pancreatitis recurrente ocurre en el 15-35% en la edad pediátrica. Se define como 2 o más episodios distintos de pancreatitis aguda con normalización de enzimas pancreáticas entre cada episodio. Una de sus causas es la pancreatitis autoinmune. En los últimos 10 años se contro...
ABSTRACT: Type 1 autoimmune pancreatitis is a cause of chronic pancreatitis related to the systemic disease known as IgG4-related Sclerosing Disease. Case report: We report the case of a 64-year-old male patient who presented recurrentepigastric pain radiating to the ...
Autoimmune pancreatitis is uncommon, responds to steroids and is usually associated with diabetes mellitus. We report a 73 year-old male who, two months after a diagnosis of diabetes mellitus, presented with obstructive jaundice and weight loss. Abdominal magnetic resonance imaging was suggestive of an a...
Pancreatitis Autoinmune/complicaciones,
Pancreatitis Autoinmune/tratamiento farmacológico,
Complicaciones de la Diabetes/complicaciones,
Complicaciones de la Diabetes/tratamiento farmacológico,
Diabetes Mellitus/tratamiento farmacológico,
Glucocorticoides/uso terapéutico,
Prednisona/uso terapéutico,
Pancreatitis Autoinmune/diagnóstico por imagen,
Hipoglucemiantes/uso terapéutico,
Inmunoglobulina G/sangre,
Insulina/uso terapéutico,
Imagen por Resonancia Magnética,
Resultado del Tratamiento
We report a 63-year-old male patient who consulted for a 4-month history of xerophthalmia, xerostomia
and cervicalgia, associated with jaundice, choluria, low weight and night sweats. Exams show an obstructive pattern and abdominal ultrasound describes a possible mass in the pancreatic head with secondar...
Navarro, Erika-Paola;
Suso, Juan-Pablo;
Chamorro, Magali;
Hormaza, Andrés;
Echeverri, Alex;
Posso-Osorio, Iván;
Bonilla-Abadía, Fabio;
Escobar-Stein, Juliana;
Cañas, Carlos A;
Bravo, Juan Carlos;
Tobón, Gabriel J.
RESUMEN La enfermedad relacionada con IgG4 es una condición inflamatoria sistémica, caracterizada por la infiltración de diversos órganos por complejos formados por células plasmáticas IgG4 positivas, asociadas con niveles elevados de IgG4 en el suero. El diagnóstico de esta enfermedad es complejo...
Autoimmune pancreatitis (AIP) is an inflammatory disease of the pancreas. The mechanism of the disease
is not completely known. However, AIP shows cellular and humoral immunity elements, the most important being helper and regulatory T lymphocytes as well as B-lymphocytes and plasmocytes, participating
i...
A doença sistêmica associada à IgG4 pode acometer virtualmente todos os órgãos, o que torna seu diagnóstico diferencial bastante abrangente. A pancreatite autoimune foi a primeira lesão orgânica a ser associada à IgG4 e, apenas em 2003, manifestações extrapancreáticas foram descritas. Portant...
