Pachyonychia congenita with an unusual intraoral manifestation: case report
J. Oral Diagn; 9 (), 2024
Pachyonychia congenita (PC) is a rare dermatosis impacting skin structures, appendages, and mucous membranes, primarily characterized by nail dystrophy, palmoplantar keratoderma, and plantar pain. Oral manifestation are particularly natal teeth and oral leukokeratosis and may be the earliest clinical sig...