Heterotaxy syndrome with agenesis of dorsal pancreas and diabetes mellitus: case report and review of the literature
Arch. endocrinol. metab. (Online); 63 (4), 2019
SUMMARY Heterotaxy syndrome (HS) is a rare congenital condition with multifactorial heritance, characterized by an abnormal arrangement of thoraco-abdominal organs and vessels. Patients present with multiple cardiac, gastrointestinal, hepatosplenic, pancreatic, renal, neurological and skeletal disorders ...