Abstract Pierre Robin Sequence (PRS) is a congenital condition characterized by micrognathia, glossoptosis, and cleft palate that presents with airway obstruction and developmental delay with or without other congenital anomalies. These patients' anesthesia management is challenging because of difficult ...
Pierre Robin sequence (PRS) is a condition consisting of three essential components:
micrognathia or retrognathia, cleft palate, and glossoptosis. It can be part of multiple
congenital anomalies. We present the case and outcome of a 3-month-old clinically
stable patient who has PRS with Dandy-Walker vari...
La secuencia de Pierre Robin (SPR) es una enfermedad rara, caracterizada por una tríada de malformaciones orofaciales como retrognatia, glosoptosis y fisura velopalatina media (paladar hendido); las cuales, generalmente provocan obstrucción de la vía aérea (OVA). La corrección de los defectos palati...
Pierre Robin sequence is a set of congenital conditions characterized by the presence of micrognathia, glossoptosis, cleft palate and obstruction of the airways. The latter can lead to many other complications such as respiratory difficulties, apnea, weight loss and even death. Currently, mandibular dist...
ABSTRACT Background: This study investigated the association of Robin Sequence with ABO and RhD blood group phenotypes. Methods: A retrospective cross-sectional study was performed of a cohort of Robin Sequence patients of the Hospital de Reabilitação de Anomalias Craniofaciais - Universidade de São...
RESUMO Objetivo: identificar os diagnósticos de enfermagem em lactentes com Sequência de Robin isolada. Método: estudo descritivo desenvolvido em um hospital especializado em anomalias craniofaciais e síndromes relacionadas, no período de novembro de 2015 a março de 2016. Participaram 20 lactente...
ABSTRACT Objective: to report the nurses' experience in relation to the training of caregivers of infants with Isolated Robin Sequence (IRS) for maintaining care after hospital discharge from the perspective of Self-Care Theoretical Framework. Method: the following categories were considered in this ex...
Entre los niños que nacen con falta de fusión de la bóveda palatina, un número
determinado corresponde a recién nacidos con síndrome de Pierre Robin. Aquí
se abre un abanico de pacientes con un grado variable de complejidades y anomalías. Algunos que portan otros síndromes aún más complejos, q...
Fisura del Paladar/complicaciones,
Fisura del Paladar/patología,
Síndrome de Pierre Robin/patología,
Síndrome de Pierre Robin/terapia,
Procedimientos Quirúrgicos Operativos/métodos,
Colgajos Quirúrgicos/trasplante,
Micrognatismo/cirugía,
Micrognatismo/patología,
Insuficiencia Velofaríngea/patología,
Disfonía/terapia,
Cuidados Posteriores
ABSTRACT Purpose To describe the speech of a patient with Pierre Robin Sequence (PRS) and severe speech disorders before and after participating in an Intensive Speech Therapy Program (ISTP). Methods The ISTP consisted of two daily sessions of therapy over a 36-week period, resulting in a total of 360 ...
Introdução: Pierre Robin, em 1923, descreveu a sequência das malformações e as correlacionou com os sinais clínicos de insuficiência
respiratória, o que trouxe a constatação da necessidade de tratamento, muitas vezes urgente. A conduta terapêutica deve ser individualizada
para cada caso e resp...
