Erdheim-Chester disease after Essential Thrombocythemia: coincidence or not?
Hematol., Transfus. Cell Ther. (Impr.); 45 (1), 2023
Results: 17
Hiperpigmentação Mucocutânea Associada à Terapia de Hidroxiureia em Paciente com Trombocitemia Essencial: Relato de Caso
Mucocutaneous Hyperpigmentation Associated with Hydroxyurea Therapy in a Patient with Essential Thrombocythemia: Case Report
Rev. Bras. Cancerol. (Online); 69 (1), 2023
Introdução: A hiperpigmentação mucocutânea é uma condição dermatológica que pode estar relacionada a tratamentos quimioterápicos,
a exemplo das terapias com uso de hidroxiureia (HU). A HU é um fármaco citostático de amplo uso nas doenças mieloproliferativas e
compõe a principal linha de tr...
Estudio de mutaciones en neoplasias mieloproliferativas Philadelphia negativas en un hospital público chileno
Rev. med. Chile; 150 (7), 2022
BACKGROUND: Philadelphia negative myeloproliferative neoplasms (Ph-MPN) are clonal disorders whose pathogenesis has been elucidated in recent years, creating diagnostic and prognostic algorithms. AIM: To study JAK2, CALR y MPL gene mutations in patients with Ph-MPN. MATERIALS AND METHODS: Descriptive cro...
Manejo anestésico de pacientes con trombocitemia esencial
Anesthetic management of a patient with essential trombocythemia
Rev. cuba. anestesiol. reanim; 20 (3), 2021
La trombocitemia esencial forma parte del grupo de neoplasias mieloproliferativas. Se caracteriza por síntomas microvasculares y vasomotores, recuento plaquetario superior a 450 x 109/l, proliferación megacariocítica con morfología grande y madura, ausencia de proliferación eritroide y granulocític...
Características clínicas y epidemiológicas de las neoplasias mieloproliferativas Philadelphia negativas en el sistema público de salud de Chile
Rev. méd. Chile; 149 (11), 2021
BACKGROUND: Philadelphia-negative myeloproliferative neoplasms (Ph-MPN) are chronic hematological disorders characterized by the overproduction of one or more mature myeloid blood cell lineages. Classical Ph-MPN are polycythemia vera (PV), essential thrombocytopenia (ET) and primary myelofibrosis (PMF). ...
Chile/epidemiología, Janus Quinasa 2/genética, Mutación, Trastornos Mieloproliferativos/diagnóstico, Trastornos Mieloproliferativos/epidemiología, Trastornos Mieloproliferativos/genética, Policitemia Vera/diagnóstico, Policitemia Vera/epidemiología, Policitemia Vera/genética, Mielofibrosis Primaria/diagnóstico, Mielofibrosis Primaria/epidemiología, Mielofibrosis Primaria/genética, Trombocitemia Esencial/diagnóstico, Trombocitemia Esencial/genética
Intracardiac thrombosis in essential thrombocythemia
Rev. colomb. anestesiol; 48 (4), 2020
Patients with Essential Thrombocythemia pose a variety of anesthetic challenges including a heightened risk of perioperative thrombosis. This condition is also associated with perioperative hemorrhage, risk for developing heparin induced thrombocytopenia type 2 during cardiac surgery and digital gangrene...
Clinical and molecular profile of a Brazilian cohort of patients with classical BCR-ABL1-negative myeloproliferative neoplasms
Hematol., Transfus. Cell Ther. (Impr.); 42 (3), 2020
ABSTRACT Background: The classical BCR-ABL1-negative myeloproliferative neoplasms (MPNs) are Polycythemia Vera (PV), Essential Thrombocythemia (ET) and Primary Myelofibrosis (PMF). In developing countries, there are few reports that truly reveal the clinical setting of these patients. Therefore, we aime...
Trombose essencial: uma revisão da literatura
Rev. bras. anal. clin; 52 (1), 2020
Trombose essencial é uma das doenças mieloproliferativas crônicas, rara e de etiologia ainda desconhecida, mas que apresenta risco alto de eventos trombóticos e/ou hemorrágicos, uma vez que acomete as células megacariocíticas e, consequentemente, as plaquetas. O objetivo deste trabalho foi realiza...
Calidad de vida en pacientes con neoplasias mieloproliferativas crónicas Filadélfia negativas
Acta méd. colomb; 44 (2), 2019
Resumen Introducción: la carga sintomática de pacientes con neoplasias mieloproliferativas crónicas Filadélfia negativas (NMC-PhN) afecta la calidad de vida (CV). Existen escalas para evaluar la magnitud de los síntomas, una de ellas, MPN-SAF-10. En nuestra región existe escasa información sobre ...
Essential thrombocythemia - a predisponent factor for stroke
Rev. Assoc. Med. Bras. (1992, Impr.); 65 (6), 2019
SUMMARY The essential thrombocythemia is one of the seven described forms of myeloproliferative neoplasms. It is characterized by megakaryocytic hyperplasia with consequent thrombocytosis maintained in the peripheral blood, favoring the occurrence of thrombo-hemorrhagic phenomena. We present the case of ...