The authors present the case of a patient with a 46, XX ovotesticular disorder of sex development diagnosed only in adulthood.[1] Cases like this one always result in a challenge for the treating team, as all treatment needs to be individualized. Since the 2005 Chicago consensus for disorders of sex development (DSD), the importance of a standardized terminology has become of significant relevance.[2] From an academic point of view, using the same technical terminology reduces confusion and helps the compilation of data for future studies. Authors fail to use standard terminology despite having the consensus as a reference. The frequency of these conditions makes management very challenging, and it is important to have specialized transdisciplinary teams, as this may improve the quality of care for these patients.[3] [4] [5] The authors present the chronological management for this patient, and it would be interesting to know the evolution and support given to the patient, from a psychosocial perspective, after surgery.[6] It would also be interesting to include in the discussion the rationale for the second laparotomy and how this was discussed with the patient.