In this paper we report on the dermatoglyphic patterns analyzed in a family representing the first and, to our knowladge, only familial case Mounier-Kuhn syndrome. When compared with a control sample, the dermatoglyphic patterns of the family exhibited signification differnces only in palmar and digital dermopapillary patterns, with a consequent decrease in Total Ridge Count values. This, however, could be due to the small size of the sample or may represent a trait of the family studied