CONTEXT:

Patients with Alport's syndrome (causing 5 percent of end-stage renal disease) have a higher risk of heart conduction abnormalities.

OBJECTIVE:

To report a case of Alport's syndrome developing complete atrioventricular block during renal transplantation.

CASE REPORT:

A 21-year-old man with chronic renal failure due to Alport's syndrome was submitted to a renal transplantation under epidural anesthesia and, during the intraoperative period, a complete atrioventricular block was diagnosed and promptly treated with a transcutaneous pacemaker. This extensive sympathetic block can contribute towards disturbances in the heart conduction system, particularly in patients with chronic renal disease in hemodialysis. Even in patients with a normal preoperative electrocardiogram or no conduction system disturbances, some degree of atrioventricular block, including complete atrioventricular block, can occur. In this situation, a transcutaneous pacemaker provides rapid and effective treatment in the operating room, thereby permitting the planning of a definitive treatment