Blastic plasmacytoid dendritic cell neoplasm (BPDCN) is a rare, clinically aggressive hematologic malignancy that most commonly manifests as cutaneous lesions with or without bone marrow involvement and leukemic dissemination. The demonstration of tumor cells with the characteristic immunophenotype with ...
ABSTRACT CONTEXT: Boerhaave syndrome consists of spontaneous longitudinal transmural rupture of the esophagus, usually in its distal part. It generally develops during or after persistent vomiting as a consequence of a sudden increase in intraluminal pressure in the esophagus. It is extremely rare in c...
Alventosa Mateu, Carlos;
Plana Campos, Lydia;
Larrey Ruíz, Laura;
Acedo Mayordomo, Raquel;
Sanchís Artero, Laura;
Peño Muñoz, Laura;
Núñez Martínez, Paola Concepción;
Castillo López, Génesis Aurora;
Latorre Sánchez, Mercedes;
Urquijo Ponce, Juan José;
Diago Madrid, Moisés;
Sempere García-Argüelles, Javier.
La leptospirosis es una enfermedad causada por la espiroqueta Leptospira. Se trata de una zoonosis de distribución mundial, con predominio en los trópicos. En España no es frecuente pero sí se observan casos en zonas más húmedas o con presencia de ríos, lagos o estanques, como son Cataluña, Andal...
Abstract Background: Adult T-cell Leukemia/Lymphoma (ATLL) is classified as a peripheral CD4+ T-cell neoplasm caused by the human T-cell lymphotropic virus type 1 (HTLV-1). Typical symptoms are associated with leukemic infiltration; however, atypical and exaggerated manifestations of verrucous carcinom...
Carcinoma Verrugoso/diagnóstico,
Virus Linfotrópico T Tipo 1 Humano/aislamiento & purificación,
Leucemia-Linfoma de Células T del Adulto/diagnóstico,
Protocolos de Quimioterapia Combinada Antineoplásica/uso terapéutico,
Linfocitos T CD4-Positivos,
Carcinoma Verrugoso/etiología,
Ciclofosfamida/uso terapéutico,
Doxorrubicina/uso terapéutico,
Ensayo de Inmunoadsorción Enzimática,
Resultado Fatal,
Leucemia-Linfoma de Células T del Adulto/tratamiento farmacológico,
Leucemia-Linfoma de Células T del Adulto/virología,
Prednisona/uso terapéutico,
Factores de Riesgo,
Vincristina/uso terapéutico
Abstract: Langerhans cell histiocytosis is rare and more frequent in children. The skin is affected in 50% of the cases and is the only site in 10%. Its course varies from self-limited and localized forms to severe multisystemic forms. Congenital cases are usually exclusively cutaneous and self-limited, ...
Abstract Diffuse cutaneous melanosis is a rare complication of metastatic melanoma related to a worse prognosis. There are few cases reported in the literature. Its pathogenesis has not been completely elucidated, although studies have suggested certain mechanisms for its occurrence. It is clinically man...
Biopsia,
Resultado Fatal,
Neoplasias Hepáticas/patología,
Neoplasias Pulmonares/patología,
Melaninas/orina,
Melanoma/complicaciones,
Melanoma/patología,
Melanoma/secundario,
Melanosis/etiología,
Melanosis/patología,
Melanosis/orina,
Piel/patología,
Neoplasias Cutáneas/complicaciones,
Neoplasias Cutáneas/patología,
Neoplasias Cutáneas/secundario
Abstract This case report describes an uncommon manifestation of histoplasmosis on the soft palate. The importance of appropriate treatment and follow-up in complex cases is emphasized, especially in patients with chronic diseases. Oral lesions may occur as multiple, granular and painful ulcers, as well ...
Antifúngicos/uso terapéutico,
Biopsia,
Resultado Fatal,
Histoplasmosis/tratamiento farmacológico,
Histoplasmosis/patología,
Itraconazol/uso terapéutico,
Úlceras Bucales/tratamiento farmacológico,
Úlceras Bucales/microbiología,
Úlceras Bucales/patología,
Paladar Blando/microbiología,
Paladar Blando/patología
Spontaneous bacterial peritonitis (SBP) is a frequent and severe complication in cirrhotic patients. Listeria
monocytogenes is a rare cause of SBP, which should be suspected in individuals with impaired immunity
such as advanced liver disease and inadequate response to standard antibiotic therapy. We rep...
Introducción: Las enfermedades peroxisomales son un grupo de trastornos monogénicos que incluyen desórdenes en la biogénesis del peroxisoma o deficiencias enzimáticas. La Condrodisplasia Rizomélica Punctata Tipo 1 (RCDP1) pertenece al primer grupo, es autosómica recesiva originada por mutaciones d...
