Abstract Light chain deposition disease (LCDD) is a rare clinical entity characterized by the deposition of light chain immunoglobulins in different tissues and primarily affects the kidneys, followed by the liver and heart. This disease often manifests as nephrotic syndrome with marked proteinuria and r...
ABSTRACT Introduction: Intra-articular injection of corticosteroids (IIC) for treatment of patients with juvenile idiopathic arthritis (JIA) is increasingly used in Pediatric Rheumatology. Objectives: To describe the clinical course of patients undergoing IIC in our Pediatric Rheumatology Unit. Method...
Abstract Lupus tumidus is considered a rare subtype of chronic cutaneous lupus erythematosus, characterized by erythema and bright urticarial erythematous-violaceous lesions that leave no scars after regression. Histopathology reveals perivascular and periannexal lymphohistiocytic infiltrates in the papi...
Abstract Eosinophilic fasciitis is a rare sclerodermiform syndrome of unknown etiology. It is characterized by the thickening of the muscular fascia and subcutaneous tissue, with a variable infiltration of eosinophils. Peripheral eosinophilia, poly or monoclonal hypergammaglobulinemia and increased eryth...
Eosinofilia/patología,
Fascitis/patología,
Piel/patología,
Biopsia,
Eosinofilia/tratamiento farmacológico,
Extremidades/patología,
Fascitis/tratamiento farmacológico,
Glucocorticoides/uso terapéutico,
Imagen por Resonancia Magnética,
Metilprednisolona/uso terapéutico,
Quimioterapia por Pulso,
Síndrome
Neuromyelitis optica (NMO) is a severe demyelinating disease of the central nervous system, which preferentially attacks the optic nerve and spinal cord. It is associated with antibodies against aquaporin 4. Morbidity and mortality are higher than in multiple sclerosis and its treatment focuses on immuno...
Lupus Eritematoso Sistémico/complicaciones,
Neuromielitis Óptica/complicaciones,
Antirreumáticos/uso terapéutico,
Ciclofosfamida/uso terapéutico,
Glucocorticoides/uso terapéutico,
Lupus Eritematoso Sistémico/tratamiento farmacológico,
Metilprednisolona/uso terapéutico,
Neuromielitis Óptica/tratamiento farmacológico,
Paresia/complicaciones,
Paresia/tratamiento farmacológico,
Rituximab/uso terapéutico,
Espasmo/complicaciones,
Espasmo/tratamiento farmacológico
La púrpura de Schönlein-Henoch (PSH) es una vasculitis de pequeños vasos con depósito de inmunocomplejos de IgA. La presentación en adultos es rara y grave. Los casos comunicados de PSH en pacientes infectados por HIV son escasos. Los anticuerpos anticitoplasma de neutrófilos (ANCA), detectados por...
Abstract Graft-versus-host disease (GVHD) is a major complication of allogeneic hematopoietic stem cell transplants (allo-HSCT) associated with significant morbidity and mortality. The earliest and most common manifestation is cutaneous graft-versus-host disease. This review focuses on the pathophysiolog...
Clemente, Gleice;
Hilário, Maria Odete;
Len, Claudio;
Silva, Clovis A;
Sallum, Adriana M;
Campos, Lúcia M;
Sacchetti, Silvana;
Santos, Maria Carolina dos;
Alves, Andressa Guariento;
Ferriani, Virgínia P;
Sztajnbok, Flávio;
Gasparello, Rozana;
Oliveira, Sheila Knupp;
Lessa, Marise;
Bica, Blanca;
Cavalcanti, André;
Robazzi, Teresa;
Bandeira, Marcia;
Terreri, Maria Teresa.
ABSTRACT Objective: To describe the clinical and angiographic characteristics of Takayasu's arteritis in Brazilian children and adolescents. Methods: A retrospective data collection was performed in 71 children and adolescents followed in 10 Brazilian reference centers in Pediatric Rheumatology. The ev...
Abstract Sarcoidosis is a disease which still has uncertain etiology. Possible environmental causes are cited in the literature, like organic and inorganic particles and infectious agents. Recent studies have demonstrated the occurrence of sarcoidosis in patients with chronic C hepatitis; however, this a...
Antiinflamatorios/uso terapéutico,
Colchicina/uso terapéutico,
Glucocorticoides/uso terapéutico,
Hepatitis C Crónica/tratamiento farmacológico,
Prednisona/uso terapéutico,
Sarcoidosis/tratamiento farmacológico,
Hepatitis C Crónica/complicaciones,
Reacción en Cadena de la Polimerasa,
Sarcoidosis/etiología,
Sarcoidosis/patología,
Resultado del Tratamiento
Abstract Thyroid disorders and chronic use of corticosteroids are common in the surgical population, so is necessary an appropriate perioperative management of these patients. There is no contraindication for elective surgery in patients with asymptomatic hypothyroidism and good control, it is not necess...
Enfermedades de la Tiroides/tratamiento farmacológico,
Glucocorticoides/uso terapéutico,
Periodo Perioperatorio,
Corticoesteroides/uso terapéutico,
Complicaciones Intraoperatorias/prevención & control,
Complicaciones Posoperatorias/prevención & control,
Hipotiroidismo/tratamiento farmacológico,
Hipertiroidismo/tratamiento farmacológico,
Cuidados Preoperatorios/métodos,
Insuficiencia Suprarrenal/prevención & control,
Procedimientos Quirúrgicos Operativos/métodos,
Enfermedades de la Tiroides/complicaciones
